ABSTRACT
Behçet’s disease (BD) is a systemic vasculitis, while myelodysplastic syndrome (MDS) is a heterogeneous group of clonal hematologic disorders characterized by ineffective hematopoiesis. Some studies suggest a relationship between MDS and BD, especially intestinal BD, and trisomy 8 seems to play an important role in both diseases. The presence of trisomy 8 is thought to be related to the intestinal involvement of BD. Here, we presented a case with the coexistence of intestinal BD, MDS, and trisomy 8.
Keywords:
Behçet’s disease, myelodysplastic syndrome, trisomy 8
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